Generalized odontodysplasia in a 5-year-old patient with Hallermann-Streiff syndrome: clinical aspects, cone beam computed tomography findings, and conservative clinical approach.

Autor: Damasceno JX; PhD student, Postgraduate Program in Dentistry, Federal University of Ceará, Fortaleza, Ceará, Brazil., Couto JL; PhD student, Postgraduate Program in Dentistry, Federal University of Ceará, Fortaleza, Ceará, Brazil., Alves KS; PhD student, Postgraduate Program in Dentistry, Federal University of Ceará, Fortaleza, Ceará, Brazil., Chaves CM Jr; Associate Professor, Division of Orthodontics and Pediatric Dentistry, Department of Clinical Dentistry, Federal University of Ceará, Fortaleza, Ceará, Brazil., Costa FW; Adjunct Professor, Division of Oral Radiology, Department of Clinical Dentistry, Federal University of Ceará, Fortaleza, Ceará, Brazil., Pimenta Ade M; Adjunct Professor, Division of Oral Radiology, Department of Clinical Dentistry, Federal University of Ceará, Fortaleza, Ceará, Brazil., Fonteles CS; Associate Professor, Division of Orthodontics and Pediatric Dentistry, Department of Clinical Dentistry, Federal University of Ceará, Fortaleza, Ceará, Brazil. Electronic address: cfontele@ufc.br.
Jazyk: angličtina
Zdroj: Oral surgery, oral medicine, oral pathology and oral radiology [Oral Surg Oral Med Oral Pathol Oral Radiol] 2014 Aug; Vol. 118 (2), pp. e58-64. Date of Electronic Publication: 2014 May 12.
DOI: 10.1016/j.oooo.2014.04.013
Abstrakt: This article aims to report the main clinical aspects, cone beam computed tomography (CBCT) findings, and conservative oral rehabilitation in a child born from a consanguineous marriage who presented with Hallermann-Streiff syndrome (HSS) and generalized odontodysplasia. A 5-year-old girl presented with a diagnosis of HSS for oral evaluation. Radiographically, all teeth showed wide pulp chambers and roots with thin dentinal walls and open apices, resembling ghost teeth and indicating a diagnosis of odontodysplasia. Oral rehabilitation consisted of partial dentures that were regularly adjusted to conform the device with the pattern of growth and development of the child. CBCT scan provided great insight into HSS, allowing a detailed view of the morphologic aspects and associated trabecular bone pattern. Treatment of these 2 rare conditions in young children must consider the stage of growth and development. Although extremely rare in HSS, odontodysplasia should be investigated and conservatively managed in young children.
(Copyright © 2014 Elsevier Inc. All rights reserved.)
Databáze: MEDLINE