[Intrathoracic giant peripheral nerve sheath tumor during Von Recklinghausen disease].

Autor: Ngabou UD; Service de chirurgie viscérale et thoracique, hôpital d'instruction des armées Omar Bongo-Ondimba, BP 20404, Libreville, Gabon. Electronic address: ngabou12@yahoo.fr., Mounguengui D; Service de pneumologie, hôpital d'instruction des armées Omar Bongo-Ondimba, BP 20404, Libreville, Gabon., Owono Mbouengou JP; Service de chirurgie viscérale et thoracique, hôpital d'instruction des armées Omar Bongo-Ondimba, BP 20404, Libreville, Gabon., El Wali A; Service de réanimation, hôpital d'instruction des armées Omar Bongo-Ondimba, BP 20404, Libreville, Gabon., Nguema Edzang B; Service d'imagerie médicale, hôpital d'instruction des armées Omar Bongo-Ondimba, BP 20404, Libreville, Gabon., Boguikouma JB; Service de pneumologie, hôpital d'instruction des armées Omar Bongo-Ondimba, BP 20404, Libreville, Gabon., Tchoua R; Service de réanimation, hôpital d'instruction des armées Omar Bongo-Ondimba, BP 20404, Libreville, Gabon., Aziz NE; Service d'imagerie médicale, hôpital d'instruction des armées Omar Bongo-Ondimba, BP 20404, Libreville, Gabon.
Jazyk: francouzština
Zdroj: Revue de pneumologie clinique [Rev Pneumol Clin] 2014 Jun; Vol. 70 (3), pp. 181-4. Date of Electronic Publication: 2013 Nov 05.
DOI: 10.1016/j.pneumo.2013.08.006
Abstrakt: We report the case of a patient aged 23, admitted for bilateral intrathoracic tumor, including a giant right. Surgery was performed by right sternothoracotomy. After 7 days, she presented an irreversible cardiac arrest. The malignant peripheral nerve sheath tumors are rare and aggressive. Their incidence is 0.001% in the general population and 0.16% in patients with neurofibromatosis type 1. These tumors are characterized by their risk of recurrence and poor prognosis. The treatment is the surgical resection. We analyze incidence, diagnosis and prognosis of these tumors.
(Copyright © 2013 Elsevier Masson SAS. All rights reserved.)
Databáze: MEDLINE
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