Gastroschisis and the risk of short bowel syndrome: outcomes and counselling.
| Autor: | Wood SJ; Royal Manchester Children's Hospital, Manchester, UK., Samangaya RA, Gillham JC, Morabito A |
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| Jazyk: | angličtina |
| Zdroj: | Neonatology [Neonatology] 2014; Vol. 105 (1), pp. 5-8. Date of Electronic Publication: 2013 Oct 31. |
| DOI: | 10.1159/000351038 |
| Abstrakt: | Background: Gastroschisis can be associated with short bowel syndrome (SBS). We present 4 cases with significant bowel shortening with very different ante- and postnatal presentations. Cases: Three of the cases demonstrated 'vanishing' gastroschisis with progressively worsening antenatal intra-abdominal bowel dilatation with no defect present at birth. The fourth case followed an uneventful course antenatally but developed SBS considered secondary to gastroschisis-related atresia and necrosis. All 4 cases were classified as having SBS and were enrolled within the paediatric Intestinal Rehabilitation Programme. This involves autologous gastrointestinal reconstruction following a period of bowel expansion with concomitant parenteral and enteral nutrition. Discussion: These cases demonstrate that the serious complication of significant bowel loss cannot always be anticipated. Early multidisciplinary discussion with the parents enables a shared understanding of potential outcomes. It can aid the recognition of 'vanishing' gastroschisis enabling expedient investigations and early intervention, minimising morbidity and maximising bowel length. (© 2013 S. Karger AG, Basel.) |
| Databáze: | MEDLINE |
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