[Pleura solitary fibrous tumor associated with Doege-Potter Syndrome].
Autor: | Valenzuela Membrives M; San Cecilio Klinikum, Sektion Pneumologie, Granada, Spanien. marivalen8@hotmail.com, Cassini Gómez de Cádiz L, Cueto Ladròn de Guevara A, García Pacheco M |
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Jazyk: | němčina |
Zdroj: | Pneumologie (Stuttgart, Germany) [Pneumologie] 2013 Jun; Vol. 67 (6), pp. 340-3. Date of Electronic Publication: 2013 Jun 07. |
DOI: | 10.1055/s-0033-1344079 |
Abstrakt: | The Doege-Potter Syndrome is known as a combination of intrathoracic tumor associated to symptomatic hypoglycemia. Solitary Fibrous Tumor is a mesenchymal neoplasm. Initially, it was described in the pleura, however, it starts out in any organ or tissue at the expense of a stromal CD34+ cell. Most of the patients are asymptomatic at the time of diagnosis. Symptoms such as cough, dyspnea, chest pain, and hypoglycemia due to production of IGF-2 have been reported (Doegge- Potter Syndrome). Others described paraneoplastic profiles are hypertrophic osteoarthropathy and in some cases galactorrhea. We report on a case of a 77 year old patient with solitary fibrous tumor in the pleura as well as symptomatic hypoglycemia. The primary treatment is surgical resection, and a longtime monitoring is necessary because recurrences can occur even after a long period of remission. (© Georg Thieme Verlag KG Stuttgart · New York.) |
Databáze: | MEDLINE |
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