| Autor: |
Mellara Tde S; School of Dentistry, University of São Paulo at Ribeirão Preto, Brazil., Azevedo DT, Faria G, Nelson Filho P, Queiroz AM, Brentegani LG |
| Jazyk: |
angličtina |
| Zdroj: |
Journal of dentistry for children (Chicago, Ill.) [J Dent Child (Chic)] 2012 Sep-Dec; Vol. 79 (3), pp. 176-80. |
| Abstrakt: |
Mucopolysaccharidosis type IIIB (MPS IIIB) is an autosomal recessive disorder caused by deficiency of the lysosomal enzyme a-N-acetylglucosaminidase. Affected subjects present developmental delay, attention deficit disorder, uncontrollable hyperactivity, and aggressive behavior, followed by progressive dementia and death in late adolescence. The purpose of this paper is to report the dental findings and treatment in a child with MPS IIIB. His primary molars and permanent mandibular incisors presented obliterated pulp chambers and root canals, which may be a clinical manifestation of this disorder. |
| Databáze: |
MEDLINE |
| Externí odkaz: |
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