[Prion diseases].
Autor: | Stoĭda NI, Zavalishin IA |
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Jazyk: | ruština |
Zdroj: | Zhurnal nevrologii i psikhiatrii imeni S.S. Korsakova [Zh Nevrol Psikhiatr Im S S Korsakova] 2012; Vol. 112 (9 Pt 2), pp. 59-63. |
Abstrakt: | Prion diseases are a family of progressive neurodegenerative disorders caused by prions. There are four human prion diseases: Creutzfeldt-Jakob disease, Gerstmann-Straussler-Scheinker syndrome, fatal insomnia and Kuru. They can arise in three different ways: acquired, familial or sporadic. We review clinical presentations, pathophysiology, morphological picture, diagnostic procedures and available treatment options of prion diseases. |
Databáze: | MEDLINE |
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