| Autor: |
Ota M; Department of Rheumatology and Applied Immunology, Faculty of Medicine, Saitama Medical University, Japan., Sakamoto M, Sato K, Yoshida Y, Funakubo Asanuma Y, Akiyama Y, Yamakawa M, Mimura T |
| Jazyk: |
angličtina |
| Zdroj: |
Internal medicine (Tokyo, Japan) [Intern Med] 2012; Vol. 51 (19), pp. 2825-30. Date of Electronic Publication: 2012 Oct 01. |
| DOI: |
10.2169/internalmedicine.51.8233 |
| Abstrakt: |
We treated a 77-year-old woman with pleural and pericardial effusion and ascites. Initially, collagen vascular disease was suspected due to the presence of anti-centromere antibodies and suspected complication of pulmonary arterial hypertension. However, soft-tissue abnormalities surrounding the bilateral kidneys detected on computed tomography (CT) and symmetrical lesions of the long bones detected on bone scintigraphy made us consider a diagnosis of Erdheim-Chester disease (ECD), which is a rare form of histiocytosis. We immunochemically analyzed the cells derived from the ascites in detail and confirmed the diagnosis. Immunocytochemical analyses may therefore help to achieve a better understanding of the pathogenesis of this rare disease. |
| Databáze: |
MEDLINE |
| Externí odkaz: |
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