| Autor: |
Datta G; Department of cardiology, ICVS, SSKMH, Kolkata., Dastidar DG, Kundu S, Datta B, Dastidar NG, Bannerjee A |
| Jazyk: |
angličtina |
| Zdroj: |
The Journal of the Association of Physicians of India [J Assoc Physicians India] 2011 Nov; Vol. 59, pp. 738-40. |
| Abstrakt: |
Primary ciliary dyskinesia (PCD) is an autosomal recessive heterogeneous group of conditions with variable clinical findings like recurrent respiratory tract infections, bronchiectasis, situs inversus, singly or in various combinations. Development of Pulmonary arterial hypertension can be a late complication of this disease. Here we present a case of PCD with recurrent respiratory tract infections, bronchiectasis and severe PAH, who responded to treatment with Oxygen, IV broad spectrum antibiotics and oral sildenafil. |
| Databáze: |
MEDLINE |
| Externí odkaz: |
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