[Do you know this syndrome? Piloleiomyoma].

Autor: Jaime TJ; Hospital Naval Marcílio Dias, Rio de Janeiro, Brazil. thaisjerez@yahoo.com.br, Jaime TJ, Melo DF, Guaraldi Bde M, Bastos Júnior Cde S, Lerer C
Jazyk: portugalština
Zdroj: Anais brasileiros de dermatologia [An Bras Dermatol] 2011 Nov-Dec; Vol. 86 (6), pp. 1222-9.
DOI: 10.1590/s0365-05962011000600033
Abstrakt: Piloleiomyoma, a benign smooth-muscle tumor arising from the arrectores pilorum muscles of the skin, affects males and females in the third decade of life. It presents as asymmetrical, reddish-brown nodules or papules with a firm consistency, predominantly located on the limbs. When multiple lesions are present, they may be tender or painful. Their association with uterine fibroids, referred to as Reed syndrome or familial leiomyomatosis cutis et uteri, is rare and may be associated with renal cell carcinoma. The approach consists of surgical excision in cases presenting few lesions and pharmacological treatment if symptomatic. The present paper describes a case of Reed syndrome in which a decision was made to monitor the patient in view of the absence of symptoms.
Databáze: MEDLINE