Ictal video-polygraphic features of perioral myoclonia with absences.

Autor: d'Orsi G; Epilepsy Center-Clinic of Nervous System Diseases, University of Foggia, Riuniti Hospital, Foggia, Italy. giudorsi@yahoo.it, Demaio V, Trivisano M, Pascarella MG, Specchio LM
Jazyk: angličtina
Zdroj: Epilepsy & behavior : E&B [Epilepsy Behav] 2011 Jul; Vol. 21 (3), pp. 314-7. Date of Electronic Publication: 2011 May 14.
DOI: 10.1016/j.yebeh.2011.03.040
Abstrakt: There have been few case reports of perioral myoclonia with absences (POMA) because of the lack of video-polygraphic recordings clarifying the electroencephalogram (EEG)-electromyogram (EMG) correlations. We describe one of the first video-polygraphic studies of POMA in a patient who underwent repeated and prolonged split-screen video-polygraphic recordings. The ictal EEG showed generalized and irregular discharges of spikes or multiple spikes and slow waves, while two concomitant EMG patterns appeared: (1) a rhythmic enhancement of the orbicularis oris and masseter muscles on both sides with minimal asymmetry corresponding to perioral movements, and (2) a progressive increment in muscular tone in the mylohyoideus muscle corresponding to oroalimentary automatisms. Myoclonic jerks were inconstantly time-locked to the spike component of the spike-wave complex. The evidence of a complex pattern of activation of the facial muscles suggests that the involvement of subcortical central pattern generators, related to masticatory activity, through the disinhibitory effect of the spike-wave discharge is a possible pathophysiological mechanism underlying POMA.
(Copyright © 2011 Elsevier Inc. All rights reserved.)
Databáze: MEDLINE
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