| Autor: |
Karakayali F; Department of General Surgery, Faculty of Medicine, Baskent University, 5 Sokak No: 48, Bahçelievler, Ankara, Turkey., Basaran C, Soy EA, Karakus S, Yabanoglu H, Moray G, Haberal M |
| Jazyk: |
angličtina |
| Zdroj: |
Surgery today [Surg Today] 2010; Vol. 40 (2), pp. 154-7. Date of Electronic Publication: 2010 Jan 28. |
| DOI: |
10.1007/s00595-008-4008-z |
| Abstrakt: |
We report a case of Klippel-Trenaunay syndrome (KTS) with serious morbidity caused by the rupture of hemangiomas of the spleen and inferior epigastric artery (IEA). A 40-year-old woman, who had suffered from edema and varicose veins in her left leg and toes since birth, underwent emergency laparotomy and splenectomy for a spontaneous splenic rupture. Pathological examination revealed hemangiomatosis of the spleen. She presented again 40 days later with a rectus muscle hematoma, which computed tomography revealed to be actively bleeding. Arteriography confirmed a bleeding IEA, which was then embolized. Hematological investigation revealed a heterozygous form of factor VIII and fibrinogen deficiency. The patient recovered well and was asymptomatic at her 1-year follow-up. We report this case to reinforce that investigations for KTS should involve all organ systems, and include detailed hematologic tests. By defining coagulation and vascular abnormalities, life-threatening bleeding episodes may be prevented. |
| Databáze: |
MEDLINE |
| Externí odkaz: |
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