Pentalogy of Fallot and cardiac paraganglioma: a case report.

Autor: Gabhane SK; Department of Pathology, Mahatma Gandhi Institute of Medical Sciences, Sevagram, Wardha - 442102, Maharashtra, India., Gangane NM, Sinha RT
Jazyk: angličtina
Zdroj: Cases journal [Cases J] 2009 Dec 23; Vol. 2, pp. 9392. Date of Electronic Publication: 2009 Dec 23.
DOI: 10.1186/1757-1626-2-9392
Abstrakt: Primary cardiac tumors are rare. Of these the majorities are benign and about 75% are atrial myxomas. One of the rarest tumors affecting the heart is a cardiac paraganglioma. We report an unusual case of a left ventricular paraganglioma discovered during autopsy in a 22-year female patient, a case of sudden death. This patient also had coexistent Pentalogy of Fallots along with transposition of pulmonary trunk to the left ventricle, a very rare congenital cyanotic heart disease. Chronic hypoxia due to congenital cyanotic heart disease is supposed to be the cause of development of paraganglioma in heart in these patients.
Databáze: MEDLINE