| Autor: |
Koshy A; Department of Gastroenterology, Lakeshore Hospital and Research Centre, Kochi, India. koshyabe@yahoo.com, Ramesh H, Mahadevan P, Mukkada RJ, Francis VJ, Chettupuzha AP, Mathew PG, Cyriac J, Augustine P |
| Jazyk: |
angličtina |
| Zdroj: |
Indian journal of gastroenterology : official journal of the Indian Society of Gastroenterology [Indian J Gastroenterol] 2009 May-Jun; Vol. 28 (3), pp. 107-8. Date of Electronic Publication: 2009 Nov 12. |
| DOI: |
10.1007/s12664-009-0038-8 |
| Abstrakt: |
A 2(1/2)-year-old boy presented with pruritus and jaundice of 2 weeks duration. On investigation, serum total bilirubin was 23.4 mg/dL and gamma glutamyl transpeptidase was normal. Liver biopsy was consistent with progressive familial intrahepatic cholestasis (PFIC). A partial external biliary diversion (PEBD) was done. Pruritus disappeared, growth improved and serum total bilirubin became normal, 2 months after surgery. This is the first report from India, of PFIC treated with PEBD and suggests that PEBD should be considered in patients with PFIC even if bridging fibrosis is present. |
| Databáze: |
MEDLINE |
| Externí odkaz: |
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