Portal hypertension and intrahepatic cholestasis in hepatic amyloidosis.

Autor: Zeijen RN; Department of Internal Medicine, University Hospital Maastricht, The Netherlands., Sels JP, Flendrig JA, Arends JW
Jazyk: angličtina
Zdroj: The Netherlands journal of medicine [Neth J Med] 1991 Jun; Vol. 38 (5-6), pp. 257-61.
Abstrakt: Despite the fact that hepatic involvement is frequently seen in systemic amyloidosis, major clinical symptoms or impaired hepatic functional capacity are rare. We describe a patient with primary hepatic amyloidosis, severe intrahepatic cholestasis and portal hypertension, a combination previously reported only three times in the literature. In case of an unexplained intrahepatic cholestasis or portal hypertension the possibility of amyloidosis should be considered and a Congo red staining should be performed.
Databáze: MEDLINE