Giant cell lesions with a Noonan-like phenotype: a case report.
| Autor: | Cancino CM; Porto Alegre, RS, Brazil. marcelaforerocancino@hotmail.com, Gaião L, Sant'Ana Filho M, Oliveira FA |
|---|---|
| Jazyk: | angličtina |
| Zdroj: | The journal of contemporary dental practice [J Contemp Dent Pract] 2007 May 01; Vol. 8 (4), pp. 67-73. Date of Electronic Publication: 2007 May 01. |
| Abstrakt: | Aim: The purpose of this article is to describe a case of multiple giant cell lesions of the mandible that occurred in a 14-year-old girl with phenotypic characteristics associated with Noonan Syndrome (NS). Background: NS is a dysmorphic disorder characterized by hypertelorism, short stature, congenital heart defects, short and webbed neck, skeletal anomalies, and bleeding diathesis. Report: A 14-year-old girl with a previous diagnosis of NS (sporadic case) presented with multiple radiolucent lesions in the body and ramus of her mandible. Summary: In terms of clinical behavior and the described radiographic characteristics, giant cells lesions with Noonan-like phenotype can be considered a form of cherubism. Therefore, surgical intervention is not necessary, but radiographic follow-up and observation is very important during the control and gradual regression of the lesions. |
| Databáze: | MEDLINE |
| Externí odkaz: |
|