Choledochal cyst and duodenal atresia: a rare combination of malformations.

Autor: Sugimoto T; Second Department of Surgery, Yamagata University School of Medicine, Iida-Nishi, Yamagata 990-9585, Japan., Yamagiwa I, Obata K, Ouchi T, Takahashi R, Suzuki R, Shimazaki Y
Jazyk: angličtina
Zdroj: Pediatric surgery international [Pediatr Surg Int] 2004 Sep; Vol. 20 (9), pp. 724-6. Date of Electronic Publication: 2004 Aug 20.
DOI: 10.1007/s00383-002-0783-6
Abstrakt: A rare case of congenital duodenal atresia (DA) associated with a choledochal cyst (CC) is reported. At 38 weeks of gestation, a 1,610-g girl was born by cesarean section with a prenatal diagnosis of congenital DA. After the disease was confirmed by radiographs, she underwent a duodenoduodenostomy for complete separation of the duodenum with an annular pancreas. Thirty-two months after the initial operation, she developed upper abdominal pain and acholic stools. Abdominal ultrasonography demonstrated a CC and dilated intrahepatic bile ducts. Magnetic resonance cholangiopancreatography showed an anomalous arrangement of the choledochus and the main pancreatic duct. A diffusely dilated extrahepatic bile duct was resected, and a hepaticoduodenostomy was performed after a cholecystectomy. The patient was discharged without complications. We could not find a similar case report in the English literature. Although it is not reported that there is a close relation of DA and CC in embryologic development, the presence of this combination should be considered.
Databáze: MEDLINE