| Autor: |
Hulsebos RG; Department of Surgery, University Hospital Groningen, Groningen, The Netherlands., Zeebregts CJ, de Langen ZJ |
| Jazyk: |
angličtina |
| Zdroj: |
Journal of pediatric surgery [J Pediatr Surg] 2004 Sep; Vol. 39 (9), pp. 1426-7. |
| DOI: |
10.1016/j.jpedsurg.2004.05.024 |
| Abstrakt: |
Congenital umbilical hernias in Hurler's syndrome (mucopolysaccharidosis I) are generally treated conservatively, because complications such as incarceration are, rare, and risks involved in surgical correction are high. This case report describes the surgical management of a ruptured umbilical hernia in a 3-year-old child with Hurler's syndrome. Emergency repair of the hernia was performed with primary closure of the fascia; hernia recurrence 6 months later was treated laparoscopically using a PTFE mesh graft with no evidence of re-recurrence. In selected cases of Hurler's syndrome (warning signs of rupture) elective surgical hernia repair may be indicated. |
| Databáze: |
MEDLINE |
| Externí odkaz: |
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