Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia
| Autor: | Andrew W. Wang, Kimberly Newton, Karen Kling |
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| Jazyk: | angličtina |
| Rok vydání: | 2017 |
| Předmět: | |
| Zdroj: | Case Reports in Surgery, Vol 2017 (2017) |
| Druh dokumentu: | article |
| ISSN: | 2090-6900 2090-6919 |
| DOI: | 10.1155/2017/9348461 |
| Popis: | We describe the rare instance of concomitant biliary atresia and alpha-1-antitrypsin deficiency and the first documented successful portoenterostomy in this scenario. The potential for dual pathology must be recognized and underscores that prompt diagnosis of biliary atresia, despite concomitant alpha-1-antitrypsin deficiency, is essential to afford potential longstanding native liver function. |
| Databáze: | Directory of Open Access Journals |
| Externí odkaz: |
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