Inflammatory Myofibroblastic Tumour of the Skull Base
| Autor: | Jean-Philippe Maire, Sandrine Eimer, François San Galli, Valérie Franco-Vidal, Sigolène Galland-Girodet, Aymeri Huchet, Vincent Darrouzet |
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| Jazyk: | angličtina |
| Rok vydání: | 2013 |
| Předmět: | |
| Zdroj: | Case Reports in Otolaryngology, Vol 2013 (2013) |
| Druh dokumentu: | article |
| ISSN: | 2090-6765 2090-6773 71097457 |
| DOI: | 10.1155/2013/103646 |
| Popis: | Inflammatory myofibroblastic tumors (IMTs) are rare benign clinical and pathological entities. IMTs have been described in the lungs, abdomen, retroperitoneum, and extremities but rarely in the head and neck region. A 38-year-old man presented with headache, right exophthalmia, and right 6th nerve palsy. A CT scan revealed enlargement of the right cavernous sinus and osteolytic lesions of the right sphenoid and clivus. MR imaging showed a large tumor of the skull base which was invading the sella turcica, right cavernous sinus, and sphenoidal sinus. A biopsy was performed and revealed an IMT. Corticosteroids were given for 3 months but were inefficient. In the framework of our pluridisciplinary consultation, fractionated conformal radiotherapy (FRT) was indicated at a low dose; 20 Gy in 10 fractions of 2 Gy over 12 days were delivered. Clinical response was complete 3 months after FRT. Radiological response was subtotal 6 months after FRT. Two years later, the patient is well. |
| Databáze: | Directory of Open Access Journals |
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