Progressive symmetric eritrocarotodermia Gottron: A rare case
| Autor: | M. M. Tlish, N. L. Sycheva, N. A. Boyko, M. E. Shavilova, F. A. Psavok |
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| Jazyk: | English<br />Russian |
| Rok vydání: | 2019 |
| Předmět: | |
| Zdroj: | Vestnik Dermatologii i Venerologii, Vol 95, Iss 3, Pp 40-45 (2019) |
| Druh dokumentu: | article |
| ISSN: | 0042-4609 2313-6294 |
| DOI: | 10.25208/0042-4609-2019-95-3-40-45 |
| Popis: | The article deals with ethiopathogenetic factors of origin of progredient symmetric erythrokeratodermia of Gottron which is mainly characterized by autosomal dominant mode of inheritance and is classified as a disorder of cornification with extra epidermal cellular proliferation.Clinicopathologic criteria on the basis of which this pathology can be verified are described here, such as: onset of a disease at an early age, strictly divided polycyclic, fixed, hyperkeratotic plaques with a narrow erythematic crown and a clean-cut, sometimes hyper pigmented edge, which are symmetrically located on skin on head, buttocks, limbs and are not prone to quick peripheral growth; large frequency of palmoplantar keratoderma and also histological changes typical of erythrokeratodermia.The article describes a rare clinical case of autosomal-recessive progredient symmetric erythrokeratodermia of Gottron which is distinguished by seasonal changes of skin pathological process — emergence of rash in winter and complete remissions in summer. |
| Databáze: | Directory of Open Access Journals |
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