A chylothorax in a young woman: The difficulties of medical management

Autor: Eleanor C. Barton, Simon Johnson, Neil Collin, Nidhi Bhatt, Nick A. Maskell
Jazyk: angličtina
Rok vydání: 2024
Předmět:
Zdroj: Respirology Case Reports, Vol 12, Iss 2, Pp n/a-n/a (2024)
Druh dokumentu: article
ISSN: 2051-3380
DOI: 10.1002/rcr2.1303
Popis: Abstract Lymphangioleiomyomatosis is a rare pulmonary disease affecting women of childbearing age. Whilst chylothorax is a well‐recognized complication of the condition, management strategies aren't well‐defined, have low success rates and are often only available at tertiary or specialist centres. We describe a case of a young woman referred to pleural clinic with a chylous effusion found to be secondary to lymphangioleiomyomatosis. Initial medical management was unsuccessful and recurrent drainages caused significant complications. Remission was ultimately achieved with a combination of mTOR inhibitors and interventional radiology techniques.
Databáze: Directory of Open Access Journals
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