Autor: |
Eleanor C. Barton, Simon Johnson, Neil Collin, Nidhi Bhatt, Nick A. Maskell |
Jazyk: |
angličtina |
Rok vydání: |
2024 |
Předmět: |
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Zdroj: |
Respirology Case Reports, Vol 12, Iss 2, Pp n/a-n/a (2024) |
Druh dokumentu: |
article |
ISSN: |
2051-3380 |
DOI: |
10.1002/rcr2.1303 |
Popis: |
Abstract Lymphangioleiomyomatosis is a rare pulmonary disease affecting women of childbearing age. Whilst chylothorax is a well‐recognized complication of the condition, management strategies aren't well‐defined, have low success rates and are often only available at tertiary or specialist centres. We describe a case of a young woman referred to pleural clinic with a chylous effusion found to be secondary to lymphangioleiomyomatosis. Initial medical management was unsuccessful and recurrent drainages caused significant complications. Remission was ultimately achieved with a combination of mTOR inhibitors and interventional radiology techniques. |
Databáze: |
Directory of Open Access Journals |
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