A Rare Case of Nephrotic Syndrome in the Setting of Sjogren Syndrome-related Cryoglobulinemic Vasculitis
| Autor: | Zoi Alexakou, Katerina Damianaki, Emelina Stambolliu, Dimitrios Kourniotis, Margarita Mpora, Dimitrios Petras |
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| Jazyk: | angličtina |
| Rok vydání: | 2023 |
| Předmět: | |
| Zdroj: | Saudi Journal of Kidney Diseases and Transplantation, Vol 34, Iss 3, Pp 265-269 (2023) |
| Druh dokumentu: | article |
| ISSN: | 1319-2442 2320-3838 93940661 |
| DOI: | 10.4103/1319-2442.394001 |
| Popis: | Cryoglobulinemia is a rare entity which frequently occurs in the setting of an underlying disease, with chronic hepatitis C virus infections and primary Sjogren syndrome being the most common underlying conditions. Cryoglobulinemic vasculitis (CV) is an immune-mediated type of small-vessel vasculitis with a broad spectrum of specific organ involvement, including renal, pulmonary, peripheral nerve, and cutaneous involvement and variable manifestations that can be life threatening. Moreover, a strong relationship between cryoglobulinemia and CV, with the future development of lymphoma, is well established. We present the case of a 72-year-old Caucasian male referred for nephrotic syndrome and acute renal injury. A diagnosis of Sjogren syndrome-associated CV was made, and he was successfully treated with rituximab and plasma exchange sessions. |
| Databáze: | Directory of Open Access Journals |
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