[Anti-laminin 332 mucous membrane pemphigoid with irreversible ocular and tracheobronchial involvement : Delayed diagnosis of a severe autoimmune bullous disease]

Autor: F M, Syring, D, Zillikens, E, Schmidt, M, Kasperkiewicz
Jazyk: němčina
Rok vydání: 2019
Předmět:
Zdroj: Der Hautarzt; Zeitschrift fur Dermatologie, Venerologie, und verwandte Gebiete. 70(5)
ISSN: 1432-1173
Popis: A 53-year-old man presented with a 37-year history of erosive and scarring mucosal lesions of several organs. An initial diagnosis of Stevens-Johnson syndrome was maintained for many years. Due to late correct diagnosis of an anti-laminin 332 mucous membrane pemphigoid and the fact that early, targeted, intensified immunosuppressive therapy was not initiated, the disease led to almost complete loss of vision and obstruction of airways.
Databáze: OpenAIRE