[Infantile hepatic cholestatis: An unusual case of Langerhans cells histiocytosis associated with advanced fibrosis]

Autor: Vicent, Martínez I Cózar, Margarita, Llavador Ros, Montserrat, Évole Buselli, María Del Mar, Andrés Moreno, Begoña, Polo Miquel, Judith, Pérez Rojas
Rok vydání: 2018
Předmět:
Zdroj: Revista espanola de patologia : publicacion oficial de la Sociedad Espanola de Anatomia Patologica y de la Sociedad Espanola de Citologia. 55(1)
ISSN: 1988-561X
Popis: Neonatal cholestasis is a clinical metabolic alteration requiring investigation of its eitiology. It is characterized by elevation of liver enzymes with cholestasis pattern and, in some cases, with acute liver failure. Its etiology is variable although the most frequent cause is atresia of extrahepatic bile ducts. We present a case of a 23-month-old boy who presented with cholestasis and was finally diagnosed with systemic Langerhans cell histiocytosis.
Databáze: OpenAIRE