Intrapulmonary ectopic liver associated with scimitar syndrome
| Autor: | Sajan Koshy, Sajna V. M. Kutty, Shalini Kuruvila, M Lilly |
|---|---|
| Rok vydání: | 2017 |
| Předmět: |
Microbiology (medical)
Pathology medicine.medical_specialty intrapulmonary lcsh:QR1-502 030230 surgery lcsh:Microbiology Pathology and Forensic Medicine Pulmonary sequestration 03 medical and health sciences 0302 clinical medicine Scimitar syndrome Parenchyma lcsh:Pathology medicine Diaphragmatic hernia Ectopic liver Lung business.industry General Medicine Portal tracts respiratory system medicine.disease medicine.anatomical_structure 030228 respiratory system Hernia sac business lcsh:RB1-214 |
| Zdroj: | Indian Journal of Pathology and Microbiology, Vol 60, Iss 3, Pp 399-401 (2017) |
| ISSN: | 0377-4929 |
| DOI: | 10.4103/ijpm.ijpm_416_16 |
| Popis: | We report a case of intrapulmonary ectopic liver associated with Scimitar syndrome. A two month old male child who presented with features of congestive cardiac failure underwent extensive cardiac and radiological investigations and was diagnosed with Scimitar syndrome. He was also found to have a mass in the lower lobe of the right lung, the possibilities being either a pulmonary sequestration or a diaphragmatic hernia. As his dyspnea progressively worsened, a right lower lobectomy was performed at the age of two years. Intraoperatively, no connecting pedicle or hernia sac was seen. The resected lung specimen showed a light brown mass enclosed by the lung parenchyma and microscopy showed cords of normal hepatocytes with portal tracts. The hepatocytes were positive for Hep Par1, and bile ducts were CK 7 positive. To the best of our knowledge, this is the first reported case of an intrapulmonary ectopic liver associated with Scimitar syndrome. |
| Databáze: | OpenAIRE |
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