Dyspnea due to an uncommon vascular tumor: leiomyosarcoma of the infrahepatic vena cava inferior
| Autor: | Matthias Glanemann, Barbara Stange, Samra Gafarli, Adriana Nistor, Dorian Igna, Mathias Wagner |
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| Jazyk: | angličtina |
| Rok vydání: | 2020 |
| Předmět: |
Leiomyosarcoma
medicine.medical_specialty Arterial embolism Percutaneous lcsh:Surgery Case Report 030204 cardiovascular system & hematology Malignancy Inferior vena cava Lesion 03 medical and health sciences 0302 clinical medicine Biopsy medicine medicine.diagnostic_test business.industry lcsh:RD1-811 medicine.disease medicine.anatomical_structure Dyspnea medicine.vein 030220 oncology & carcinogenesis cardiovascular system Surgery Radiology medicine.symptom Pancreas business |
| Zdroj: | Surgical Case Reports, Vol 6, Iss 1, Pp 1-5 (2020) Surgical Case Reports |
| ISSN: | 2198-7793 |
| Popis: | Background Leiomyosarcoma (LMS) of the inferior vena cava (IVC) is a rare malignancy that originated from the smooth muscle tissue of the vascular wall. Diagnoses, as well as, treatment of the disease are still challenging and to date, a radical surgical resection of the tumor is the only curative approach. Case report We report on the case of a 49-year old male patient who presented with suddenly experienced dyspnea. Besides bilateral pulmonary arterial embolism, a lesion close to the head of the pancreas was found using CT scan, infiltrating the infrahepatic IVC. Percutaneous ultrasound-guided biopsy revealed a low-grade LMS. Intraoperatively, a tumor of the IVC was observed without infiltration of surrounding organs or distant metastases. Consequently, the tumor was removed successfully, by en-bloc resection including prosthetic graft placement of the IVC. Histological workup revealed a completely resected (R0) moderately differentiated LMS of the IVC. Conclusion LMS of the infrahepatic IVC is an uncommon tumor, which may present with dyspnea as its first clinical sign. Patients benefit from radical tumor resection. However, due to the poor prognosis of vascular LMS, a careful follow-up is mandatory. |
| Databáze: | OpenAIRE |
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