Malignant extra-adrenal pelvic paraganglioma in a paediatric patient
Autor: | Gabriel Fernando Cao, Daniel Navacchia, Julian Mendez |
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Jazyk: | angličtina |
Rok vydání: | 2017 |
Předmět: |
Tachycardia
Oncology Cancer Research medicine.medical_specialty CIENCIAS MÉDICAS Y DE LA SALUD Inmunología PAEDIATRICS Case Report Malignancy paediatrics paraganglioma 03 medical and health sciences 0302 clinical medicine Paraganglioma 030225 pediatrics Internal medicine EXTRA-ADRENAL Biopsy medicine Lymph node Pelvis MALIGNANCY medicine.diagnostic_test business.industry Dilated cardiomyopathy purl.org/becyt/ford/3.1 [https] medicine.disease Medicina Básica medicine.anatomical_structure PARAGANGLIOMA 030220 oncology & carcinogenesis extra-adrenal purl.org/becyt/ford/3 [https] Radiology medicine.symptom Differential diagnosis business malignancy |
Zdroj: | CONICET Digital (CONICET) Consejo Nacional de Investigaciones Científicas y Técnicas instacron:CONICET ecancermedicalscience |
Popis: | The extra-adrenal paraganglioma is a neoplasm originating in regional structures, uncommon in paediatrics. We report on a case of a 13-year-old patient who began with severe arterial hypertension, tachycardia, dilated cardiomyopathy and elevated levels of catecholamines in the blood and urine. The presence of a retrovesical pelvic mass in contact with the right vaginal dome was determined by imaging studies. A diagnosis of malignant extra-adrenal pelvic paraganglioma with lymph node metastases was reached through biopsy and the surgical resection of subsequent local recurrences. Paragangliomas are usually located in the paravertebral zones from the base of the skull to the retroperitoneum and are benign in 90% of cases. This kind of neoplasia is uncommon in paediatrics, especially those located in the pelvis. In cases of masses of a gynaecological origin, a differential diagnosis should be considered, and a histological and immunohistochemical study is essential in certifying the diagnosis. Fil: Cao, Gabriel Fernando. Consejo Nacional de Investigaciones Científicas y Técnicas; Argentina. Gobierno de la Ciudad de Buenos Aires. Hospital General de Niños Pedro Elizalde (ex Casa Cuna); Argentina Fil: Mendez, Julian. Gobierno de la Ciudad de Buenos Aires. Hospital General de Niños Pedro Elizalde (ex Casa Cuna); Argentina Fil: Navacchia, Daniel. Gobierno de la Ciudad de Buenos Aires. Hospital General de Niños Pedro Elizalde (ex Casa Cuna); Argentina |
Databáze: | OpenAIRE |
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