Pulmonary veno-occlusive disease. A report of four cases
| Autor: | Gerry Thompson, James W. Ironside, J S Whittaker, Carol Ward, W Kelly, P S Hasleton |
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| Rok vydání: | 1986 |
| Předmět: |
Adult
Male medicine.medical_specialty Histology Adolescent Blood Pressure Pulmonary Artery Pathology and Forensic Medicine Internal medicine medicine.artery Medicine Humans Child Lung Hepatitis business.industry Vascular disease General Medicine Middle Aged medicine.disease Thrombosis Pulmonary hypertension Blood pressure medicine.anatomical_structure Pulmonary Veins Pulmonary artery Cardiology Pulmonary Veno-Occlusive Disease Female business Lung Volume Measurements |
| Zdroj: | Europe PubMed Central |
| ISSN: | 0309-0167 |
| Popis: | Four cases of pulmonary veno-occlusive disease are described. Two patients, who were brothers, had respiratory tract infections. The third patient had chronic active hepatitis and coeliac disease suggesting an abnormality of the immune system; the fourth patient had no obvious cause but presented initially with systemic hypertension. Three of the cases had been diagnosed initially as primary pulmonary hypertension either on open lung biopsy or clinically. In all cases the pulmonary arteries were abnormal with medial hypertrophy, intimal fibrosis and, in some cases, thrombosis in elastic pulmonary arteries. These findings suggest that pulmonary veno-occlusive disease is not confined to veins and should be considered as a widespread pulmonary vascular disease. The range of aetiological factors indicate that it should not be considered as a single disease entity. |
| Databáze: | OpenAIRE |
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