Camurati-Engelmann disease: a late and sporadic case with metaphyseal involvement
| Autor: | X. L. Hamoir, P. Matthijs, M. Van Campenhoudt, P. Lambin, H. G. Brat |
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| Rok vydání: | 1999 |
| Předmět: |
Adult
Male medicine.medical_specialty Knee Joint Medullary cavity Bone and Bones Diagnosis Differential Humans Medicine Radiology Nuclear Medicine and imaging Femur Tibia Fibula business.industry Ulna Camurati–Engelmann disease Camurati-Engelmann Syndrome General Medicine Anatomy medicine.disease medicine.anatomical_structure Knee pain Blood chemistry Radiology medicine.symptom Tomography X-Ray Computed business |
| Zdroj: | European Radiology. 9:159-162 |
| ISSN: | 1432-1084 0938-7994 |
| DOI: | 10.1007/s003300050648 |
| Popis: | A 40-year-old white man with a 3-year history of mild to severe right thigh and knee pain was referred for radiographic investigation. Radiographs show a fusiform, bilaterally symmetrical enlargement of the diaphyses and metaphyses of the long bones (femur, tibia, fibula, radius and ulna). A narrowed medullary cavity is illustrated on CT scan of the femur. All bones show periosteal and endosteal bone formation. There is no history of familial involvement, trauma, infection or systemic illness. Blood chemistry could not point out any abnormality. Radiographic findings and clinical history suggest the diagnosis of Camurati-Engelmann disease, also known as progressive diaphyseal dysplasia (PDD). This case is of interest because of its rare metaphyseal involvement, mild form and sporadic presentation. |
| Databáze: | OpenAIRE |
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