Severe Respiratory Distress Syndrome Unresponsive to Intensive Care Treatment – Diagnostic and Therapeutic Considerations
| Autor: | H. G. Limbach, Ludwig Gortner, P. Fries, Ali Baghai, R. M. Bohle, Günther Löffler, Shirley Meyer, A. Hasenfus |
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| Rok vydání: | 2011 |
| Předmět: |
Lung Diseases
Male congenital hereditary and neonatal diseases and abnormalities medicine.medical_specialty Pediatrics Lymphangiectasis Cardiotocography Gestational Age Comorbidity Lymphangiectasia Kidney Surfactant therapy Fatal Outcome Pregnancy alpha 1-Antitrypsin Deficiency Intensive care medicine Humans Treatment Failure Intensive care medicine Lung Lymphatic Vessels Respiratory Distress Syndrome Newborn Alpha 1-antitrypsin deficiency Respiratory distress business.industry Myocardium Homozygote Infant Newborn respiratory system medicine.disease respiratory tract diseases Respiratory failure Infant Extremely Low Birth Weight Dysplasia Pediatrics Perinatology and Child Health Disease Progression Intensive Care Neonatal Female Respiratory Insufficiency business Complication |
| Zdroj: | Klinische Pädiatrie. 223:283-286 |
| ISSN: | 1439-3824 0300-8630 |
| DOI: | 10.1055/s-0030-1270485 |
| Popis: | Respiratory Distress Syndrome (RDS) is a common complication in preterm neonates. If RDS is not responding to conventional treatment modalities (surfactant therapy, ventilatory support, etc.), an underlying pathology (pulmonary lymphangiectasia, capillary alveolar dysplasia, alpha-1 antitrypsin deficiency, etc.) other then prematurity should be taken into consideration.Here, we report on a preterm neonate with the unusual simultaneous occurrence of pulmonary and systemic lymphangiectasia and homozygous alpha-1 antitrypsin deficiency who developed severe RDS that was refractory to conventional treatment. The diagnostic and therapeutic approach in this patient is presented. |
| Databáze: | OpenAIRE |
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