| Autor: |
Federica Lena, Chiara Pellegrino, Antonio Maria Zaccara, Maria Luisa Capitanucci, Giacomo Esposito, Barbara Daniela Iacobelli, Daniela Longo, Tamara Caldaro, Diletta Bruno, Francesca Bevilacqua, Francesca Santato, Giulia Lucignani, Carlo Efisio Marras, Enrico Castelli, Pietro Bagolan, Giovanni Mosiello |
| Rok vydání: |
2022 |
| Předmět: |
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| Zdroj: |
Pediatric Surgery International. 38:1487-1494 |
| ISSN: |
1437-9813 |
| DOI: |
10.1007/s00383-022-05186-z |
| Popis: |
Urethral duplication (UD) is a rare malformation, which can be associated with other anomalies, like anorectal malformations (ARM). ARM has been described with occult spinal dysraphism (OSD). No ARM-UD-OSD combination has been reported.To share our experience and to discuss the management of ARM-UD-OSD association.We retrospectively reviewed records of five boys with UD. Four of these had ARM-UD-OSD association. ARM was the first diagnosis in all; OSD and UD was detected during screening for associated malformation.All patients underwent ARM correction, 3 after colostomy. All reached fecal continence, 3 are performing bowel management. Three patients underwent UD surgical correction. Because of symptoms' worsening, 2 children had detethering surgery. At a mean follow-up of 9.5 years, all patients have normal renal function, 3 are on clean intermittent catheterization (CIC) for neurogenic bladder (1 has a cystostomy, another one an appendicostomy).UD and OSD should be considered in patients with ARM. Children with these conditions associated must be centralized in a third-level Center and management carefully planned; in particular, urethral reconstruction should be weighed, considering CIC could be required. Suspicion of neurogenic bladder must be present in OSD patient. |
| Databáze: |
OpenAIRE |
| Externí odkaz: |
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