Intraorbital and intracranial soft-tissue glomus tumor in an 8-year-old child

Autor: Richard C. E. Anderson, Jeffrey N. Bruce, James Garvin, Peter Canoll, Alfred T. Ogden, Michael Kazim, Neil A. Feldstein, Todd C. Hankinson
Rok vydání: 2008
Předmět:
Zdroj: Journal of Neurosurgery: Pediatrics. 1:389-391
ISSN: 1933-0715
1933-0707
Popis: ✓ Soft-tissue glomus tumors (or glomangiomas) are unrelated to neuroendocrine paragangliomas (glomus tympanicum, jugulare, and vagale). The authors present the first reported case of an orbital soft-tissue glomus tumor in a child. An 8-year-old girl developed rapidly progressive right-eye blindness, proptosis, and a sixth cranial nerve palsy. Magnetic resonance imaging demonstrated a homogeneously enhancing lesion extending from the right orbit through the superior orbital fissure to the cavernous sinus and middle cranial fossa. A biopsy specimen demonstrated the lesion to be a soft-tissue glomus tumor. Following angiography and embolization, a gross-total resection of the tumor was achieved. The patient was treated with adjuvant proton-beam radiotherapy. At 24 months follow-up her proptosis and sixth cranial nerve palsy had resolved and there was no evidence of tumor recurrence.
Databáze: OpenAIRE