Beckwith-Wiedemann Syndrome: Open bite evolution after tongue reduction
| Autor: | Jesús-Manuel Muñoz, J. Hernández-Godoy, Mercedes Martín, Estefanía Alonso-Rodríguez, Miguel Burgueño, Elena Gómez |
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| Rok vydání: | 2018 |
| Předmět: |
Male
Beckwith-Wiedemann Syndrome Adolescent medicine.medical_treatment Oral Surgical Procedures Beckwith–Wiedemann syndrome Review Drooling 03 medical and health sciences 0302 clinical medicine Tongue medicine Macroglossia Humans Phonation Child General Dentistry Reduction (orthopedic surgery) Retrospective Studies Orthodontics business.industry Open Bite Infant Retrospective cohort study 030206 dentistry Airway obstruction CIENCIAS MÉDICAS [UNESCO] medicine.disease Treatment Outcome Otorhinolaryngology Child Preschool 030220 oncology & carcinogenesis UNESCO::CIENCIAS MÉDICAS Glossectomy Female Surgery Oral Surgery medicine.symptom business |
| Zdroj: | Alonso Rodríguez, Estefanía ; Gómez García, Elena ; Martín, Mercedes ; Muñoz Caro, Jesús M. ; Hernandez Godoy, Juan ; Burgueño García, Miguel. Beckwith-Wiedemann syndrome : open bite evolution after tongue reduction. En: Medicina oral, patología oral y cirugía bucal. Ed. inglesa, 23 2 2018: 18 Medicina Oral, Patología Oral y Cirugía Bucal RODERIC. Repositorio Institucional de la Universitat de Valéncia instname |
| ISSN: | 1698-6946 |
| DOI: | 10.4317/medoral.21319 |
| Popis: | Background Macroglossia causes functional deficits such as airway obstruction, drooling, phonation difficulties, and leads to protrusion of dentoalveolar structures resulting in an anterior open bite and a prognathic mandibular appearance. Macroglossia is present in the majority of patients with Beckwith-Wiedemann syndrome (BWS) and surgical treatment may be indicated. Material and Methods A retrospective review was conducted including BWS patients who underwent surgical tongue reduction between 2000 and 2015 at the Hospital Universitario La Paz, Madrid. Results Out of 16 patients with BWS, surgery was performed in 11 cases. Tongue protrusion with open bite was the main indication for surgical treatment. Reduction glossectomy was performed using the keyhole technique. We analysed the relationship between age at surgery and evolution of open bite. Complications were minimal and satisfactory outcomes were observed with a decrease in anterior open bite. Conclusions In this study we have observed that surgical treatment in patients with BWS and open bite accompanied by macroglossia seems to provide positive results with a satisfactory outcome in dentoskeletal alterations. Key words:Macroglossia, Beckwith- Wiedemann syndrome, glossectomy; tongue reduction, malocclusion. |
| Databáze: | OpenAIRE |
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