Malignant fibrous histiocytoma arising in a patient with multiple neurofibromatosis: A case report and a literature review
| Autor: | Judith Pester, Robert G. Penn, David Allan Katz, Paul S. Johnson |
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| Rok vydání: | 1979 |
| Předmět: |
Male
Pathology medicine.medical_specialty Lung Neoplasms Neurofibromatosis 1 Lung Histiocytoma Benign Fibrous business.industry Soft tissue General Medicine Middle Aged medicine.disease Metastasis Neoplasms Multiple Primary Multiple neurofibromatosis medicine.anatomical_structure Thigh Oncology Neurofibrosarcoma medicine Humans Surgery business |
| Zdroj: | Journal of Surgical Oncology. 12:97-105 |
| ISSN: | 1096-9098 0022-4790 |
| Popis: | A case report of a 56-year-old man with the characteristic clinical and histologic features of multiple neurofibromatosis is presented. This patient was also diagnosed as having a malignant fibrous histiocytoma involving the right thigh with metastasis to the lung. A definite association between Von Reckling-hausen's disease and various sarcomas (most commonly neurofibrosarcomas) of the peripheral nerves and the somatic soft tissues is well-known. This is apparently the first report in the literature of a malignant fibrous histiocytoma arising in a patient with multiple neurofibromatosis. The phenomenon of sarcomatous change in Von Recklinghausen's disease and the clinical and pathologic features of malignant fibrous histiocytoma are also discussed. |
| Databáze: | OpenAIRE |
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