Excision of fibrous band and application of tension band plating in focal fibrocartilaginous dysplasia: A case report and literature review
Autor: | Guney Yilmaz, Sancar Bakırcıoğlu, Engin Yilmaz, Kemal Kosemehmetoglu |
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Rok vydání: | 2021 |
Předmět: |
Coxa Vara
Metaphysis Fracture Fixation Internal 03 medical and health sciences 0302 clinical medicine Fracture fixation medicine Deformity Humans Orthopedics and Sports Medicine Femur Orthopedic surgery Varus deformity 030222 orthopedics medicine.diagnostic_test business.industry Infant Magnetic resonance imaging Fibrous Dysplasia of Bone 030229 sport sciences General Medicine Anatomy medicine.disease Magnetic Resonance Imaging Radiography Treatment Outcome medicine.anatomical_structure Dysplasia Epiphysis Female Surgery medicine.symptom business RD701-811 Rare disease |
Zdroj: | Acta Orthopaedica et Traumatologica Turcica, Vol 55, Iss 2, Pp 184-188 (2021) |
ISSN: | 2589-1294 1017-995X |
DOI: | 10.5152/j.aott.2021.20080 |
Popis: | Focal fibrocartilaginous dysplasia (FFCD) is a rare disease that can cause angular deformities of long bones. The common pathologic finding is a thick fibrotic band extending from epiphysis to metaphysis on one side of the bone. The tethering effect of the fibrotic band around the growth plate is thought to be the main etiology for the development and progression of the deformity. FFCD mostly affects the proximal tibia and the distal femur. The literature contains different treatment options. Here, we present the case of a 20-month-old girl with FFCD on the medial side of the distal femur causing varus deformity. Our treatment protocol included excision of the fibrotic band from the medial side and application of a two-hole plate for guided growth on the lateral side of the distal femur. Deformity correction was achieved rapidly with no complications. A literature review is also presented along with pathologic and magnetic resonance imaging findings. |
Databáze: | OpenAIRE |
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