Giant Dermatofibrosarcoma Protuberans With Bilateral Orbital Involvement
| Autor: | Smith Ann M. Chisholm, Victor Liou, Neda Esmaili, Valentina Logunova, Robert J. Havlik |
|---|---|
| Rok vydání: | 2019 |
| Předmět: |
Adult
medicine.medical_specialty Skin Neoplasms genetic structures Biopsy Dermatofibroma Optic neuropathy 03 medical and health sciences 0302 clinical medicine Dermatofibrosarcoma protuberans medicine Humans Neoplasm Invasiveness business.industry Soft tissue sarcoma Dermatofibrosarcoma Soft tissue General Medicine medicine.disease Combined Modality Therapy Magnetic Resonance Imaging eye diseases Ophthalmology medicine.anatomical_structure Scalp 030221 ophthalmology & optometry Orbital Neoplasms Surgery Female sense organs Radiology Sarcoma Eyelid business |
| Zdroj: | Ophthalmic plastic and reconstructive surgery. 35(2) |
| ISSN: | 1537-2677 |
| Popis: | Dermatofibroma sarcoma protuberans (DFSP) is a rare, locally aggressive soft tissue sarcoma with a tendency for recurrence after excision. Although reports of unilateral orbital and bilateral eyelid disease exist, there have been no prior reports of DFSP with bilateral orbital involvement and no previously described cases of DFSP associated with transient optic neuropathy. The authors present a case report of a 34-year-old woman with a giant scalp DFSP involving the bilateral orbits. Despite radical resection with 5 cm margins where possible, multiple positive margins remained including deep positive margins at the bilateral superomedial retroseptal soft tissue. The patient completed adjuvant radiation for surgically unresectable disease. This case highlights the challenge of achieving local control given the disease extent and infiltration of the bilateral eyelids and orbits. This is the first reported case of DFSP with bilateral orbital involvement and associated transient optic neuropathy. |
| Databáze: | OpenAIRE |
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