Basal encephalocele associated with morning glory syndrome: case report
| Autor: | Paulo Imamura, Angela Maria Spinola e Castro, Adriana Aparecida Siviero Miachon, Nitamar Abdala, Ivanete Minotto, Roberto Gomes Nogueira |
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| Přispěvatelé: | Universidade Federal de São Paulo (UNIFESP) |
| Jazyk: | angličtina |
| Rok vydání: | 2007 |
| Předmět: |
Male
Fundus Oculi Optic Disk Sphenoid bone Retinography encefalocele basal Encephalocele Basal (phylogenetics) síndrome de morning glory pituitary dwarfism medicine Humans magnetic resonance imaging Child Dwarfism Pituitary Morning medicine.diagnostic_test business.industry Magnetic resonance imaging computed tomography Anatomy Syndrome medicine.disease ressonância magnética Magnetic Resonance Imaging Skull medicine.anatomical_structure Neurology nanismo hipofisário Neurology (clinical) Basal encephalocele tomografia computadorizada business Tomography X-Ray Computed basal encephalocele morning glory syndrome |
| Zdroj: | Arquivos de Neuro-Psiquiatria v.65 n.4a 2007 Arquivos de neuro-psiquiatria Academia Brasileira de Neurologia instacron:ABNEURO ResearcherID Repositório Institucional da UNIFESP Universidade Federal de São Paulo (UNIFESP) instacron:UNIFESP |
| Popis: | As encefaloceles basais são entidades raras e correspondem a herniações do tecido cerebral através de um defeito do crânio, ao longo da lâmina crivosa etmoidal ou do osso esfenoidal. A rara síndrome morning glory, com alterações de fundo de olho características pode apresentar-se associada à encefalocele basal. Deficiências hormonais hipofisárias podem ocorrer. Relatamos caso de nanismo hipofisário com encefalocele transesfenoidal de diagnóstico tardio associada à síndrome de morning glory, mostrando as alterações na retinografia, tomografia computadorizada e ressonância magnética. The basal encephaloceles refer to rare entities and they correspond to herniation of brain tissue through defects of skull along the cribiform plate or the sphenoid bone. A rare morning glory syndrome, with characteristic retinal defect has been reported in association with basal encephaloceles. Hypophysis hormonal deficiencies may occur. We accounted for a pituitary dwarfism with delayed diagnosed transsphenoidal encephalocele associated with morning glory syndrome, showing the alterations found in retinography, computed tomography and magnetic resonance imaging. UNIFESP DDI Neuroradiology Department UNIFESP DDI UNIFESP Pediatrics Endocrinology Department UNIFESP Ophthalmology Department UNIFESP, DDI Neuroradiology Department UNIFESP, DDI UNIFESP, Pediatrics Endocrinology Department UNIFESP, Ophthalmology Department SciELO |
| Databáze: | OpenAIRE |
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