Absent right superior vena cava in visceroatrial situs solitus
Autor: | Ulrike Bartram, Richard Van Praagh, Jami C. Levine, Michael H Hines, Stella Van Praagh, Andrew S. Bensky |
---|---|
Rok vydání: | 1997 |
Předmět: |
Heart Defects
Congenital Male medicine.medical_specialty Vena Cava Superior Adolescent medicine.medical_treatment law.invention law Superior vena cava Internal medicine Cardiopulmonary bypass medicine Extracorporeal membrane oxygenation Humans Abnormalities Multiple Heart Atria Child Coronary sinus Aged Heart transplantation business.industry Pulmonary artery catheter Infant Newborn Infant Arrhythmias Cardiac Middle Aged Surgery medicine.anatomical_structure Child Preschool Cardiology Female Azygos vein Cardiology and Cardiovascular Medicine business Situs solitus |
Zdroj: | The American journal of cardiology. 80(2) |
ISSN: | 0002-9149 |
Popis: | Absence of the right superior vena cava (SVC) in visceroatrial situs solitus is rare (0.07% to 0.13% of congenital cardiovascular malformations), and little is known about the type and frequency of additional heart defects and arrhythmias. We reviewed previous publications and present 9 new cases. Based on 121 known cases, we found that this anomaly is typically characterized by: (1) persistence of the left SVC draining into the right atrium by way of the coronary sinus, and (2) left-sided azygos vein draining into the left SVC. Less constant features were: (3) additional cardiovascular malformations (46%), and (4) rhythm abnormalities (36%) that usually appeared related to the complications of old age. Since absence of the right SVC is clinically silent, its status should be assessed echocardiographically prior to invasive medical or surgical procedures. This is important to avoid various management difficulties during the following procedures: (1) implantation of a transvenous pacemaker, (2) placement of a pulmonary artery catheter for intraoperative or intensive care unit monitoring without fluoroscopy, (3) systemic venous cannulation for extracorporeal membrane oxygenation, (4) systemic venous cannulation for cardiopulmonary bypass, (5) partial or total cavopulmonary anastomoses; and (6) orthotopic heart transplantation and endomyocardial biopsies. |
Databáze: | OpenAIRE |
Externí odkaz: |