Interdisciplinary approach to treat dyskeratosis congenita associated with severe aplastic anemia: A case report
| Autor: | Terezinha de Oliveira Nogueira, Paula Pinheiro de Abreu, Éfani Caroline de Freitas Banzi, Mônica Fernandes Gomes |
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| Rok vydání: | 2006 |
| Předmět: |
Male
Dentistry Dental Caries Severity of Illness Index Dyskeratosis Congenita stomatognathic system Tongue medicine Deciduous teeth Humans Aplastic anemia Dental Restoration Permanent General Dentistry Dental Care for Children Periodontal Diseases Anterior teeth integumentary system business.industry Anemia Aplastic Oral Hygiene medicine.disease Pancytopenia Dyskeratosis stomatognathic diseases Treatment Outcome Hypocellularity medicine.anatomical_structure Child Preschool Dental Care for Chronically Ill business Dyskeratosis congenita |
| Zdroj: | Special Care in Dentistry. 26:81-84 |
| ISSN: | 1754-4505 0275-1879 |
| Popis: | This paper reports on a 4-year-old male who had dyskeratosis congenita and who acquired severe aplastic anemia. The patient developed hyperpigmentation of the face, neck and chest region, arms, shoulders and legs. In addition, he had dry skin, deformed fingernails and toenails, sparse hair and eyebrows and hyperkeratosis of the dorsum of the hands and feet. Laboratory and histological analysis revealed severe pancytopenia and dyserythropoiesis of red blood cells, hypocellularity of white blood cells and decreased megakaryocytes with dysplasia. The intraoral examination identified bleeding gums; petechiae of the palate, tongue and cheek mucosa; and an atrophic, smooth and shining dorsal surface of the tongue. There were deep carious lesions in the deciduous mandibular molars and maxillary anterior teeth; as well as mobility of mandibular left canine, which had bone loss. The treatment for oral lesions included diet changes, improved oral hygiene, and extraction of the deciduous teeth destroyed by caries. |
| Databáze: | OpenAIRE |
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