Right ventricular undifferentiated pleomorphic sarcoma: A case report
| Autor: | Ronaldo Zamuco, Jared P. Beller, Scott Maddalo, Leon Axel, Abe DeAnda, Leora B. Balsam |
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| Rok vydání: | 2016 |
| Předmět: |
Cardiac tumor
medicine.medical_specialty business.industry Myxoma Sarcoma 030204 cardiovascular system & hematology medicine.disease Trunk Article Undifferentiated Pleomorphic Sarcoma Surgery 03 medical and health sciences 0302 clinical medicine Great vessels 030220 oncology & carcinogenesis Heart failure medicine Right ventricle Neoplasm Radiology business Cardiology and Cardiovascular Medicine Cardiac Tumors |
| Zdroj: | Journal of Cardiology Cases. 13(2):60-62 |
| ISSN: | 1878-5409 |
| DOI: | 10.1016/j.jccase.2015.10.008 |
| Popis: | Undifferentiated pleomorphic sarcoma (UPS), previously known as malignant fibrous histiocytoma, is a neoplasm that occurs most often in the extremities, trunk, and retroperitoneum. Rarely, UPS can occur in the cardiac chambers and great vessels. The diagnosis of UPS is difficult to establish with noninvasive imaging techniques, and these tumors may be mistaken for benign neoplasms preoperatively. Surgical excision is the standard therapy, although the extent and location of the tumor may limit the ability to perform a complete resection. Adjuvant chemotherapy and/or radiation are often used for incomplete resections.We report the case of a 57-year-old woman with a large right ventricular UPS who presented with signs of right-sided heart failure. Preoperative imaging was suggestive of a myxoma; however, histopathologic evaluation of the specimen confirmed a diagnosis of UPS. Microscopic margins of the specimen were positive, and adjuvant chemotherapy was given. We discuss diagnostic and treatment considerations for this unusual cardiac tumor. |
| Databáze: | OpenAIRE |
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