Sturge-Weber syndrome
| Autor: | Gubernath, Rajkumar Daniel, Natarajan Manivannan, Ramakrishnan Swamy Ahathya, Subramanium Gokulanathan, Shanmugasundaram |
|---|---|
| Rok vydání: | 2012 |
| Předmět: |
medicine.medical_specialty
Sturge–Weber syndrome lcsh:Analytical chemistry lcsh:RS1-441 Bioengineering Sturge-Weber syndrome ultrasound doppler Gingival Hemangioma General Biochemistry Genetics and Molecular Biology lcsh:Pharmacy and materia medica Hemangioma Lesion medicine General Pharmacology Toxicology and Pharmaceutics portwine stain lcsh:QD71-142 business.industry Leptomeninges Dental Science - Case Report Angiomatosis Hyperplasia medicine.disease Surgery stomatognathic diseases Skull medicine.anatomical_structure medicine.symptom business |
| Zdroj: | Journal of Pharmacy & Bioallied Sciences Journal of Pharmacy and Bioallied Sciences, Vol 4, Iss 6, Pp 349-352 (2012) |
| ISSN: | 0975-7406 |
| DOI: | 10.4103/0975-7406.100304 |
| Popis: | Encephalotrigeminal angiomatosis (Sturge-Weber syndrome) is a rather uncommon congenital condition characterized by the combination of venous angioma of the leptomeninges over the cerebral cortex with ipsilateral angiomatous lesions of the face, and sometimes the skull, jaws, and oral soft tissues. A case of portwine stain with intraoral gingival hemangioma is presented. There were no other systemic manifestations. Patient reported with a complaint of localized tumor-like swelling in gums. Based on the presence of sharply demarcated vascular lesion unilaterally on the face and with ipsilateral intraoral vascular hyperplasia in the lip and gingiva, a variant of encephalotrigeminal angiomatosis was diagnosed. Ultrasound Doppler flowmetry was used to determine the blood flow. Dental management included plaque control instructions, scaling, root planning, and excision of the lesion done under general anesthesia. Close follow-up and meticulous plaque control have kept the oral condition under fairly good control. |
| Databáze: | OpenAIRE |
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