| Popis: |
Abnormal arrangement of thoraco-abdominal anatomical structures and their vascular elements in association with dysmorphism, is called heterotaxia syndrome or situs ambiguous syndrome [3]. This syndrome is further dived into two main sets of anomaly bundles, on one hand bilateral left-sidedness or polysplenia syndrome and on the other hand bilateral right-sidedness or asplenia syndrome. It is viewed in literature as a spectrum ranging from situssolitus which is the normal distribution of organs to situsinvertustotalis, the mirror-image of the normal arrangement of organs inside the body and in between the twoentities, a wide range of malformations, as a result of a Disruption of axis determination during early embryonic: situs ambiguous .We are reporting a case of polysplenia syndrome discovered in a patient with only a mild diffuse abdominal pain. |
