Management Strategies for Hydrocephalus in Alobar Holoprosencephaly: A Case Report and Discussion
| Autor: | Ali Ozen, Necati Ucler, Can Sarica, Selahattin Akar, Capan Konca, Cem Seyho Yucetas |
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| Rok vydání: | 2018 |
| Předmět: |
Pediatrics
medicine.medical_specialty business.industry General Medicine medicine.disease Infant newborn Alobar holoprosencephaly Hydrocephalus Shunting 03 medical and health sciences Prosencephalon 0302 clinical medicine 030228 respiratory system Holoprosencephaly Pediatrics Perinatology and Child Health Diabetes insipidus medicine Surgery Neurology (clinical) business 030217 neurology & neurosurgery Shunt valve |
| Zdroj: | Pediatric Neurosurgery. 53:337-341 |
| ISSN: | 1423-0305 1016-2291 |
| Popis: | Holoprosencephaly is a rare congenital malformation resulting from an impaired midline division of the prosencephalon into distinct cerebral hemispheres. Hydrocephalus is a frequent problem among the few survivors with alobar holoprosencephaly (aHPE), its most severe form. The literature about neurosurgical management of hydrocephalus in this condition is limited and dispersed, and there are still some points that need to be resolved. We report the case of a newborn with aHPE, hydrocephalus, and central diabetes insipidus. We delineate the complexity of the management of these patients and emphasize the benefits of using an initial programmable shunt valve. Further discussion about management strategies includes reviewing previous reports and the benefits of shunting for hypothalamic osmoreceptor function. |
| Databáze: | OpenAIRE |
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