| Autor: |
Vera, S. R., Shokouh‐Amiri, M. H., Riely, C., Adamec, T., Jensen, S. L., Gaber, A. O. |
| Zdroj: |
Clinical Transplantation; October 1993, Vol. 7 Issue: 5 p503-507, 5p |
| Abstrakt: |
The prognosis of patients suffering from Budd‐Chiari syndrome is poor without treatment. Both medical and surgical treatments have some benefit. Surgical treatment consists cither of portosystemic shunt surgery or liver transplantation. It is still debatable which patients might benefit from either of these procedures. We report a patient with Budd‐Chiari syndrome with extensive thrombotic involvement of both systemic and portal venous systems. The Budd‐Chiari syndrome appeared acutely following a spontaneous abortion in a 33‐ycar‐old woman who was 4 weeks pregnant. The course was fulminant with acute liver failure. Thrombolytic therapy failed to resolve the inferior vena cava thrombosis. Because of the extensive and progressive involvement of both portal and cavai systems, an emergent cavai and portal vein thrombectomy followed by liver transplantation was performed. This was followed by sustained anticoagulant therapy. The patient was discharged 3 weeks after transplantation and has remained asymptomatic since February' 1991. We concluded that orthotopic liver transplantation, with portal and inferior vena cava thrombectomy, can be performed in patients with complete acute hepatocellular necrosis resulting from massive thrombosis of hepatic veins, abdominal vena cava, and portal vein. |
| Databáze: |
Supplemental Index |
| Externí odkaz: |
|
