Caroli's disease

Autor: Mercadier, M., Chigot, J. P., Clot, J. P., Langlois, P., Lansiaux, P.
Zdroj: World Journal of Surgery; February 1984, Vol. 8 Issue: 1 p22-29, 8p
Abstrakt: In 1958, Caroli [1, 2] was the first to describe congenital dilatations of intrahepatic bile ducts concerning a segment, a sector, a lobe, or both halves of the liver. Sometimes the dilatations are associated with congenital hepatic fibrosis as described in 1954 by Grumbach [3], dilatations of biliary ductules (biliary angiomatosis), and parenchymal sclerosis. This hereditary autosomal recessive disease is associated in many cases with nephrospongiosis or Cacchi-Ricci's disease [4].
Databáze: Supplemental Index