Pulmonary capillary haemangiomatosis.

Autor: Whittaker JS, Pickering CA, Heath D, Smith P
Jazyk: angličtina
Zdroj: Diagnostic histopathology [Diagn Histopathol] 1983 Apr-Jun; Vol. 6 (2), pp. 77-84.
Abstrakt: A Cypriot male of 22 years died after suffering recurrent daily haemoptyses of varying severity and slowly increasing effort intolerance for a period of four and a half years. Examination of a lung biopsy specimen revealed dilated vascular channels suggestive of a congenital anomaly of the pulmonary vasculature. Histological examination of the lung following necropsy revealed the diagnosis of pulmonary capillary haemangiomatosis. In this condition sheets of thin-walled blood vessels infiltrate the lung parenchyma, the walls of pulmonary arteries and veins, the bronchi and the pleura. The infiltration of pulmonary veins and venules induces secondary pulmonary veno-occlusive disease. This appears to be the second example of this disease which has been reported. It is open to clinical and histological mis-diagnosis and clinicians and pathologists should be aware of the existence of this entity.
Databáze: MEDLINE