Primary neuroendocrine tumour of the extrahepatic biliary duct.

Autor:	Fennelly S; General Surgery, Northern Hospital Epping, Epping, Victoria, Australia sarah.fennelly@gmail.com.; Master of Cancer Sciences, The University of Melbourne Faculty of Medicine Dentistry and Health Sciences, Melbourne, Victoria, Australia., Teoh B; Hepatobiliary Surgery, Northern Hospital Epping, Epping, Victoria, Australia., Velaga J; Radiology, Northern Hospital Epping, Epping, Victoria, Australia., Houli N; Hepatobiliary Surgery, Northern Hospital Epping, Epping, Victoria, Australia.
Jazyk:	angličtina
Zdroj:	BMJ case reports [BMJ Case Rep] 2024 Nov 11; Vol. 17 (11). Date of Electronic Publication: 2024 Nov 11.
DOI:	10.1136/bcr-2024-261745
Abstrakt:	Neuroendocrine tumours of the extrahepatic bile ducts are extremely rare, accounting for only 0.2-2% of gastrointestinal tract neuroendocrine neoplasms. Here, we present an incidental finding of this rare tumour, identified during staging scans post-resection of a malignant rectosigmoid polyp and treated with resection and biliary reconstruction. A suspicious, arterially enhancing porta hepatis lymph node was identified on CT and further investigated with liver MRI and 68Ga DOTATATE PET. These revealed a lobulated lesion of the hilum which showed marked avidity without metastases. The patient underwent a successful radical resection of the extrahepatic biliary ducts (including the left, right and common hepatic ducts), the common bile duct and hepaticojejunostomy formation. Histology revealed a 20-mm well-differentiated NET, WHO Grade 2. Two years later, the patient is alive and well without recurrence. This fascinating case illustrates the importance of thorough preoperative planning of surgical resection for tumours at an unusual primary site. Competing Interests: Competing interests: None declared. (© BMJ Publishing Group Limited 2024. No commercial re-use. See rights and permissions. Published by BMJ.)
Databáze:	MEDLINE
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