Fetal Hypoplastic Left Heart Syndrome with Intact Atrial Septum: From Successful in utero Stenting to Subtotal Stent Occlusion - A Case Report.

Autor: Tulzer A; Children's Heart Center Linz, Department of Pediatric Cardiology, Kepler University Hospital, Linz, Austria.; Medical Faculty, Johannes Kepler University Linz, Linz, Austria., Scharnreitner I; Medical Faculty, Johannes Kepler University Linz, Linz, Austria.; Institute of Feto-Maternal Medicine, Kepler University Hospital, Linz, Austria., Sames-Dolzer E; Medical Faculty, Johannes Kepler University Linz, Linz, Austria.; Children's Heart Center Linz, Department of Pediatric Cardiac Surgery, Kepler University Hospital, Linz, Austria., Kreuzer M; Medical Faculty, Johannes Kepler University Linz, Linz, Austria.; Children's Heart Center Linz, Department of Pediatric Cardiac Surgery, Kepler University Hospital, Linz, Austria., Mair R; Children's Heart Center Linz, Department of Pediatric Cardiac Surgery, Kepler University Hospital, Linz, Austria., Tulzer G; Children's Heart Center Linz, Department of Pediatric Cardiology, Kepler University Hospital, Linz, Austria.; Medical Faculty, Johannes Kepler University Linz, Linz, Austria.
Jazyk: angličtina
Zdroj: Fetal diagnosis and therapy [Fetal Diagn Ther] 2024 Oct 16, pp. 1-7. Date of Electronic Publication: 2024 Oct 16.
DOI: 10.1159/000542069
Abstrakt: Introduction: Fetuses with hypoplastic left heart syndrome (HLHS) and intact atrial septum (IAS) have an overall poor prognosis and a high risk of neonatal death due to severe secondary lung damage. Intrauterine stenting of the atrial septum was introduced in these patients to enable survival.
Case Presentation: We present a case of a HLHS fetus with IAS and signs of incipient nutmeg lung, in whom at 30 weeks gestation an atrial stent was successfully placed but continuously developed subtotal stent-obstruction over the next weeks.
Conclusion: Continuous obstruction of placed atrial septum stents until delivery is possible and requires close monitoring of successfully treated fetuses.
(© 2024 S. Karger AG, Basel.)
Databáze: MEDLINE