Retroperitoneal Peripancreatic Ganglioneuroma Encasing the Celiac Trunk and Superior Mesenteric Artery.
| Autor: | Avila-Sanchez P; Department of Hepato-Pancreato-Biliary Surgery, Instituto Nacional de Ciencias Medicas y Nutrición Salvador Zubiran, Mexico City, MEX., Barron-Cervantes NM; Department of General and Gastrointestinal Surgery, Medica Sur Hospital, Mexico City, MEX., Martinez-Esteban A; Department of General and Gastrointestinal Surgery, Fundación Clínica Medica Sur, Mexico City, MEX., Chan-Nuñez LC; Department of Hepato-Pancreato-Biliary Surgery, Instituto Nacional de Ciencias Medicas y Nutricion Salvador Zubiran, Mexico City, MEX. |
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| Jazyk: | angličtina |
| Zdroj: | Cureus [Cureus] 2024 Jan 16; Vol. 16 (1), pp. e52405. Date of Electronic Publication: 2024 Jan 16 (Print Publication: 2024). |
| DOI: | 10.7759/cureus.52405 |
| Abstrakt: | A retroperitoneal ganglioneuroma is an exceptionally rare surgical entity, even more so in pancreaticoduodenal tumors. These well-differentiated neuroepithelial tumors originate in the neural crest, emerge in the sympathetic nervous system, and consist of ganglion cells and stromal Schwann cells. Generally, these tumors, despite being mostly benign, may be associated with venous or arterial vascular involvement. The symptomatology presented will depend on the mass effect due to tumor growth, and surgical excision is the only therapeutic option offered today to these patients. However, encapsulation of the main vessels represents a great surgical complexity. Various surgical approaches have been employed throughout history; however, the current preferred method is an open midline laparotomy, involving an extensive Kocher maneuver and an artery-first approach, aiming for an R0 resection of the tumor with total vascular preservation to the greatest extent possible. We present a case of an R2 resection involving a 95 mm x 85 mm retroperitoneal peripancreatic ganglioneuroma with double vascular involvement (celiac trunk and superior mesenteric artery). The procedure utilized an artery-first approach with total vascular preservation in a 17-year-old woman who had long-standing gastrointestinal symptoms due to the mass effect. Competing Interests: The authors have declared that no competing interests exist. (Copyright © 2024, Avila-Sanchez et al.) |
| Databáze: | MEDLINE |
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