Doege-Potter syndrome: a systematic review of the literature and case presentation of a rare pelvic malignant solitary fibrous tumour.
Autor: | Kiely NP; School of Women and Children's Health, Faculty of Medicine, University of New South Wales, Sydney, New South Wales, Australia neilldiver@gmail.com.; Obstetrics and Gynaecology, The Royal Hospital for Women, Randwick, New South Wales, Australia., Sinha R; School of Women and Children's Health, Faculty of Medicine, University of New South Wales, Sydney, New South Wales, Australia.; Department of Gynaecological Oncology, Royal Hospital for Women, Randwick, New South Wales, Australia., Tang K; Department of Pathology, Prince of Wales Hospital, Randwick, New South Wales, Australia., Wan KM; School of Women and Children's Health, Faculty of Medicine, University of New South Wales, Sydney, New South Wales, Australia.; Department of Gynaecological Oncology, Royal Hospital for Women, Randwick, New South Wales, Australia. |
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Jazyk: | angličtina |
Zdroj: | BMJ case reports [BMJ Case Rep] 2021 Aug 19; Vol. 14 (8). Date of Electronic Publication: 2021 Aug 19. |
DOI: | 10.1136/bcr-2021-242447 |
Abstrakt: | Solitary fibrous tumours (SFTs) are a rare mesenchymal neoplasm with an incidence of 2.8 per 100 000 of which only 1% occur in the female genital tract. Doege-Potter syndrome is a paraneoplastic phenomenon associated with approximately 5%-10% of SFTs and is characterised by non-islet cell hypoglycaemia due to tumour production of low molecular weight insulin-like growth factor-II. We present the fourth confirmed case of female pelvic SFT with Doege-Potter syndrome and a literature review. Competing Interests: Competing interests: None declared. (© BMJ Publishing Group Limited 2021. No commercial re-use. See rights and permissions. Published by BMJ.) |
Databáze: | MEDLINE |
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